Klinische und experimentelle Kardiologie
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Abstrakt

A Case of AL Lambda Amyloidosis with Severe Cardiac Impairment Whose Outcome was Unfavorable

Hannanse Mahunan Murielle Ahodakin*, Ngardjibem Djita, Pierre Bolarin Lawani, Ibrahima Sory Sylla, Noura Feniche

Amyloidosis is an infiltrative pathology with a quasi-systemic manifestation. It can be a transthyretin infiltration (mutated or senile), a light chain AL infiltration that represents a therapeutic emergency or a type AA infiltration. The diagnosis is sometimes less obvious but is increasingly refined with tools and algorithms within the reach of practitioners. In some difficult cases, a myocardial biopsy is sometimes necessary. We report the case of one patient, followed in our cardiology department, in whom the diagnosis of AL amyloidosis was made late. Sadly, she died a few months later despite chemotherapy.