Zeitschrift für Tumorforschung
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Dermatofibrosarcoma Protuberans with a Spindle and Pleomorphic Cell High-Grade Sarcoma in the Breast: A Rare Case Report

Ali Imran Kucuk

Dermatofibrosarcoma protuberans (DFSP) is a rarely observed tumor of a subcutaneous tissue. Its incidence is about 0.8-4.5/1000000. Fibrosarcomatous transformation of DFSP has been described in the literature, accounting for about 10% of DFSP cases. A high-grade sarcoma with fusiform and pleomorphic cells is a very rarely observed tumor. It is mainly located on proximal extremities and body; it is seldomly seen in the breast. The tumor grows gradually within the years. The local recurrence is frequently observed, however, the metastasis is rarely present. It is treated by a resection with free surgical margins. We presented Forty-three years old multipar patient a case of DFSP with a high-grade sarcoma, a histologic feature with spindle and pleomorphic cells in the breast. Up to date, on no cases with such a tumor in the breast has not been reported yet.