Klinische und experimentelle Kardiologie
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Abstrakt

Ebstein´s Anomaly Associated with Left Heart Malformations: Presentation of Two Cases and Review of the Literature

Nilda Espinola-Zavaleta*, Guadalupe Hernández-Pacheco, Luis Muñoz-Castellanos, Leonel Avendaño-Pérez and Gabriela Meléndez- Ramírez

Introduction: Ebstein´s anomaly is a rare congenital cardiac malformation. This anomaly is seen as part of a generalized disturbance in the development of the right ventricle and, in some cases, of the left ventricle.
Case presentation: We present two adult women with this anomaly; both with mitral valve regurgitation, one of them with prolapse of the anterior leaflet and the other one with cleft of the anterior mitral leaflet, and the last one have also bicuspid aortic valve, aortic coarctation, persistence of ductus arteriosus and ostium secundum atrial septal defect.
Conclusion: The non-invasive imaging techniques such as echocardiography and cardiac magnetic resonance imaging play a very important role in the diagnosis, prognosis and treatment of these patients. An understanding of the morphological and functional details of Ebstein‘s anomaly is the most important point for the correct interpretation of the noninvasive images and adequate clinical judgment. Finally, it is mandatory to assess the left cavities of the heart in all patients with Ebsteins anomaly, in order to establish a complete evaluation.